Applying Ecology of Human Performance Model in Spinal Muscular Atrophy Disease: A Case Report

Document Type : Case Report

Authors

1 Department of Occupational Therapy, Zanjan University of Medical Sciences, Zanjan, Iran

2 Assistant Professor Department of Occupational Therapy, School of Rehabilitation Sciences, Iran University of Medical Sciences, Tehran, Iran

3 Assistant Professor, Department of Occupational Therapy, School of Rehabilitation Sciences, Iran University of Medical Sciences, Tehran, Iran

Abstract

Background and aim: Nowadays, due to the wide variety of models and applying these models in different areas of the field, occupational therapy can have an important role in providing rehabilitation services to patients. In this case, one of the proposed models that has a variety of roles in environmental accommodations is Ecology of Humane Performance (EHP) model. Applying this model is the appropriate intervention in progressive disorders like neuromuscular disease. The purpose of the present study was applying the strategies of EHP model in a family with 3 members suffering from Spinal Muscular Atrophy type 3 (SMA3).
Case Report: The present case report is about a family with 6 members, (4 children and the parents who have a family relationship). This family has 4 children (2 girls and 2 boys) 3 of whom (2 sons, 1 daughter) are diagnosed with SMA3.
Results: Using EHP model in this family, significant results in the field of functional mobility, quality of life, life satisfaction, and driving were obtained in such a way that family members were satisfied with their treatments.

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Main Subjects

References

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The Scientific Journal of Rehabilitation Medicine
Volume 6, Issue 2
July and August 2017
Pages 298-305

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History

  • Receive Date: 08 February 2016
  • Revise Date: 23 July 2016
  • Accept Date: 07 August 2016
  • First Publish Date: 22 June 2017

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