Quality of Life in Patients with Retinitis Pigmentosa in Shiraz

Document Type : Original article

Authors

1 Student Research Committee, MSc in Optometry, School of Rehabilitation, Shahid Beheshti University of Medical Science, Tehran, Iran

2 Department of Optometry, School of Rehabilitation, Shahid Beheshti University of Medical Science, Tehran, Iran

3 Associate Professor, Department of Ophthalmology, School of Medicine, Baqiyatallah University of Medical Science, Tehran, Iran

4 Associate Professor, Department of Ophthalmology, School of Medicine, Shiraz University of Medical Science, Shiraz, Iran

5 MSc in Biostatistics, Basic Sciences Department, School of Rehabilitation, Shahid Beheshti University of Medical Science, Tehran, Iran

Abstract

Background and Aim: Retinitis Pigmentosa (RP) is a group of hereditary retinal degenerative diseases, causing blindness among individuals younger than 60 years, and patients have to continue with visual impairment for their entire lives, which can cause changes on their quality of life. The purpose of the present study was to determine the vision-related quality of life using the National Eye Institute Visual Function Questionnaire-25 (NEI VFQ-25) in patients with RP, and to examine the relationship between quality of life and visual acuity.
Materials and Methods: The present cross-sectional study included 35 patients with RP (18 male, 17 female) with the mean age of 37.57±11.42 and 35 normal participants for control (18 male, 17 female) with the mean age of 36.11±9.32. Best Corrected Visual Acuity (BCVA) sores were measured in distance and near. Participants answered the Persian version of the NEI VFQ-25. The difference between RP and normal group and the correlation between quality of life and visual acuity were determined.
Results: The mean NEI VFQ-25 scores were 47.59±18.72 in RP patients and 92.29±5.48 in normal controls. This difference was highly significant (P<0.001). Also, among RP patients, there was a significant correlation between the mean NEI VFQ-25 score and BCVA, according to Log MAR scale (r= - 0.704, P<0.001).
Conclusion: Retinitis pigmentosa and decreased visual acuity have a great impact on the quality of life.
 

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Main Subjects


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Volume 6, Issue 4
January and February 2018
Pages 168-174
  • Receive Date: 07 September 2016
  • Revise Date: 06 December 2016
  • Accept Date: 10 January 2017
  • First Publish Date: 22 December 2017