تأثیر یک برنامه تمرین اصلاحی متقارن بر ناهنجاری اسکولیوز در فرد مبتلا به سندرم شبه‌مارفان (مطالعه موردی)

ساده دل فدافن, زهرا; غنی زاده حصار, نرمین

doi:10.32598/SJRM.13.6.3242

تأثیر یک برنامه تمرین اصلاحی متقارن بر ناهنجاری اسکولیوز در فرد مبتلا به سندرم شبه‌مارفان (مطالعه موردی)

نوع مقاله : گزارش مورد

نویسندگان

گروه فیزویولوژی ورزشی و حرکات اصلاحی، دانشکده علوم ورزشی، دانشگاه ارومیه، ارومیه، ایران.

10.32598/SJRM.13.6.3242

چکیده

مقدمه و اهداف سندرم مارفان یک اختلال ارثی است که تشخیص آن بر مبنای یافته‌های کلینیکی در سیستم‌های قلبی‌عروقی، بینایی، اسکلتی‌عضلانی و تاریخچه فامیلی مثبت است. بیماران شبه‌مارفان اغلب، علائم و ناهنجاری‌های اسکلتی‌عضلانی مربوط به سندرم مارفان را دارند، اما مشکلات و عوارض سیستم‌های قلبی‌عروقی و بینایی را ندارند. برای این بیماران انجام ورزش و فعالیت بدنی توصیه شده است. بنابراین هدف این پژوهش بررسی تأثیر یک برنامه تمرین اصلاحی متقارن بر ناهنجاری اسکولیوز یک بیمار شبه‌مارفان بود.
مواد و روش‌ها این تحقیق از نوع مطالعه موردی بود که طی آن، 1 نفر آزمودنی مبتلا به سندرم شبه‌مارفان به مدت 12 هفته (24 جلسه) تمرینات اصلاحی متقارن را انجام داد. قبل و بعد از تمرینات زاویه کلی قوس‌های اسکولیوز به شیوه کوب در نواحی توراکس و لومبار روی عکس رادیوگرافی اندازه‌گیری شد. همچنین زاویه کوب بین مهره‌های درگیر در قوس‌های اسکولیوز با استفاده از عکس رادیوگرافی و به‌صورت سگمنت به سگمنت اندازه‌گیری شد. برای تجزیه‌و‌تحلیل داده‌ها آمارتوصیفی شامل اختلاف پیش‌آزمون و پس‌آزمون برحسب درجه و درصد استفاده شد.
یافته‌ها یافته‌ها نشان داد اندازه زاویه کوب توراکس در مقایسه پیش‌آزمون با پس‌آزمون به مقدار 3/8 درجه (15/56 درصد) و همچنین مقدار پس‌آزمون زاویه کوب لومبار نسبت به پیش‌آزمون 6/2 درجه (9/3 درصد) کاهش یافته‌اند. همچنین تغییرات زاویه کوب بین مهره‌ها نشان داد، هرچه از نقطه عطف به 2 طرف دیستال انحنای S شکل دور می‌شویم، میزان تغییرات کاهشی بیشتر می‌شود.
نتیجه گیری تمرینات اصلاحی متقارن در اصلاح زاویه کلی قوس‌های اسکولیوز و زاویه بین مهره‌ای به‌صورت موضعی تأثیر دارد. این تمرینات می‌تواند در بهبود راستای ستون فقرات افراد مبتلا به سندرم شبه‌مارفان مؤثر واقع شود.

کلیدواژه‌ها

موضوعات

آسیب شناسی ورزشی و حرکات اصلاحی

عنوان مقاله [English]

The Effect of a Symmetrical Corrective Exercise Program on the Scoliosis Deformity of A Young Male With Marfan-like Syndrome: A Case Study

نویسندگان [English]

Zahra Sadehdel Fadafan
Narmin Ghani Zadeh Hesar

Department of Exercise Physiology and Corrective Exercises, Faculty of Sports Sciences, Urmia University, Urmia, Iran.

چکیده [English]

Background and Aims Marfan syndrome is a genetic disorder that is diagnosed based on clinical findings in cardiovascular, visual and musculoskeletal systems and positive family history. Marfan-like syndrome has musculoskeletal abnormalities similar to Marfan syndrome but with no cardiovascular and visual abnormalities. Exercise and physical activity have been recommended for these patients. This study aims to investigate the effect of a symmetrical corrective exercise program on the scoliosis deformity of a a toung male patient with Marfan-like syndrome.
Methods This is a case study. The case was an 18-year-old boy with Marfan-like syndrome and scoliosis from Urmia, Iran. He performed symmetrical corrective exercises for 12 weeks (24 sessions). The Cobb angle of scoliosis curves was measured in the thoracic and lumbar regions on radiographs before and three months after the exercises. Also, the Cobb angle between the vertebrae involved in scoliosis was measured with radiographs. The degree and percentage of difference was obtained by subtracting the post-test score from the pre-test score.
Results The findings showed that the post-test thoracic angle decreased by 3.8°(15.56%) compared to the pre-test thoracic angle, and the post-test lumbar angle decreased by 6.2°(9.3%) compared to the pre-test lumbar angle. The changes in the Cobb angle between the vertebrae showed that the rate of decrease changes by moving away from the turning point to the two distal sides in the spine’s S-shaped curve.
Conclusion Symmetrical corrective exercises can reduce scoliosis curvature and the intervertebral angle and thus improve the spine alignment of people with Marfan-like syndrome.

کلیدواژه‌ها [English]

Scoliosis
Cobb’s angle
Marfan-like syndrome

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